Communication with acute intermittent porphyria patients who have tracheostomy

Authors

  • Sevda Arslan Duzce Universty
  • Özlem Altınbaş Akkaş Msc

Keywords:

Acute intermittant porphyria, tracheostomy, communication

Abstract

Objective: Introducing acute intermittent porphyria disease and investigating the communication techniques for acute intermittent porphyria patients who have tracheostomy

Case Report: 26 years old woman patient consulted to the hospital when she was 13 years old with nausea and vomiting complaints. In 2008, because of respiratory arrest, tracheostomy was implemented to the patient who had acute intermittent porphyria diagnose. The patient had two bullous lesions on the left hand and hyperpigmentation’s on the face and legs. As a result of metabolic acidosis (because of urine disease), the patient was taken to dialysis. After six months of dialysis, hypernatremia was found in the laboratory tests (Na: 85).Period of acute crisis developed In the patient with hypertension, atrophy in the muscles, fainting, abdominal pain, nausea, vomiting and diarrhea. Because of serious diarrhea, TPN was started for the patient who was fed with gavage before. Laboratory test results are Na:126, K:8.1, BUN:23.83, Urine:51, Creatinine:0.94, Leukocyte:20.4, erytrocyte:2.22, Hb:6.87g/dl, Hct: %20.9, Plt:106. 

Result: It is really difficult to communicate with these patients with lifespan limited because of an extremely severe clinical condition and tracheostomy.

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Author Biographies

Sevda Arslan, Duzce Universty

Assist.  Prof., Duzce Universty School of Health, Nursing

Özlem Altınbaş Akkaş, Msc

Duzce Universty, School of Health, nursing

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Published

2013-07-12

How to Cite

Arslan, S., & Akkaş, Özlem A. (2013). Communication with acute intermittent porphyria patients who have tracheostomy. Journal of Human Sciences, 10(2), 94–97. Retrieved from https://j-humansciences.com/ojs/index.php/IJHS/article/view/1932

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Section

Nursing and Midwifery